ISSN: 1300-0365 Dil: Türkçe
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Ocular Findings In Alport's Syndrome
Cem YIldIrIm*, Erhan Yakut**, H. İbrahim AltInsoy***
* Yrd.Doç.Dr.,Pamukkale Üniversitesi Tıp Fakültesi Göz Hastalıkları AD, Denİzlİ** Araş.Gör.Dr.,Gülhane Askeri Tıp Akademisi Göz Hastalıkları AD,*** Doç.Dr.,Gülhane Askeri Tıp Akademisi Göz Hastalıkları AD, Ankara Alport's Syndrome is a hereditary disorder of basement membrane which is characterized by nephritis with hematuria, sensory-neural deafness and ocular findings. Anterior lenticonus, lens opacities and retinal flecks are the most frequent ocular signs. A family of Alport's Syndrome whose members had bilateral anterior lenticonus and midperipheral retinal flecks is presented.Keywords: Alport's syndrome, Anterior lenticonus,
Flecked retinaTurkiye Klinikleri J Ophthalmol 1998, 7:134-136
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